early sonographic diagnosis of neurocutaneous melanosis in a newborn

Authors

zeynep ilerisoy yakut department of radiology, ankara etlik zubeyde hanim maternity and women's health academic and research hospital, ankara, turkey; department of radiology, ankara etlik zubeyde hanim maternity and women's health academic and research hospital, ankara, turkey. tel: +90-3123198908 fax: +90-3123220184

ahmet yagmur bas department of neonatology, ankara etlik zubeyde hanim maternity and women's health academic and research hospital, ankara, turkey

aynur turan department of radiology, diskapi yildirim beyazit educational and research hospital, ankara, turkey

nihal demirel department of neonatology, ankara etlik zubeyde hanim maternity and women's health academic and research hospital, ankara, turkey

abstract

neurocutaneous melanosis (ncm) is a rare, congenital non-hereditary syndrome, characterized by multiple pigmented nevi. we report the radiologic findings of a newborn who had extensive cutaneous melanotic nevus with satellite lesions in the brain. ultrasound showed multiple echogenic foci in the cerebral parenchyma. subsequent mri confirmed these lesions as characteristic deposits of melanin. the infant was asymptomatic, but presence of risk factors such as malign transformation or neurological manifestations makes early diagnosis very important. we present this case to emphasize on the radiological findings of this syndrome in order to reach an early diagnosis.

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Journal title:
iranian journal of radiology

جلد ۱۱، شماره ۴، صفحات ۰-۰

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